Data in this chapter may be updated by a Medline search using the keywords: external auditory canal, middle ear, temporal bone and skull base neoplasm. More specific searches were made on glandular tumours, adenoma, carcinoid tumour, endolymphatic sac tumours, inverted papilloma, haemangioma, haemangiopericytoma, osteoma, chordoma, chondrosarcoma, rhabdomyosarcoma and Langerhans cell histiocytosis, focusing on their presentation, diagnosis and management.