ABSTRACT

Soft-tissue sarcoma is a rare tumor in children and is considerably rarer still in the newborn period (birth to 6 weeks). Their behavior is, for the most part, benign with malignant varieties accounting for no more than 2% of all sarcomatous lesions in childhood. The very rarity of these tumors and their generally benign behavior underscore the need for a careful and balanced approach to their management. This is further emphasized by the complexity of surgery, radiotherapy, and chemotherapy in this age group, which, when weighed against the potential lifelong complications of therapy, justifies careful and measured discussion as to the most appropriate course of action.