Megacystis microcolon intestinal hypoperistalsis syndrome (MMIHS) is a rare congenital and generally fatal cause of functional intestinal obstruction in the newborn. The main characteristics for this syndrome are abdominal distension caused by a massive enlarged nonobstructed urinary bladder, microcolon, and decreased or absent intestinal peristalsis.1 MMIHS is usually associated with incomplete intestinal rotation and shortened small bowel.